Concepedia

Accumulation of human SOD1 and ubiquitinated deposits in the spinal cord of SOD1G93A mice during motor neuron disease progression correlates with a decrease of proteasome

Cristina Cheroni, Marco Peviani, Paolo Cascio, S Debiasi, C. Monti, Caterina Bendotti

Neurobiology of Disease · 2005 · 102 citations · 55 references

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References

55

Mutations in Cu/Zn superoxide dismutase gene are associated with familial amyotrophic lateral sclerosis

D.R. Rosen, Teepu Siddique, David T. Patterson et al. · Nature · 1993 · 7K citations

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Motor Neuron Degeneration in Mice that Express a Human Cu,Zn Superoxide Dismutase Mutation

Mark E. Gurney, Haifeng Pu, Arlene Y. Chiu et al. · Science · 1994 · 4.1K citations

, , +17

An adverse property of a familial ALS-linked SOD1 mutation causes motor neuron disease characterized by vacuolar degeneration of mitochondria

Philip C. Wong, Carlos A. Pardo, David Borchelt et al. · Neuron · 1995 · 1.4K citations

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ALS-Linked SOD1 Mutant G85R Mediates Damage to Astrocytes and Promotes Rapidly Progressive Disease with SOD1-Containing Inclusions

Lucie Bruijn, Mark W. Bêcher, Michael K. Lee et al. · Neuron · 1997 · 1.3K citations · Full text

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Motor neurons in Cu/Zn superoxide dismutase-deficient mice develop normally but exhibit enhanced cell death after axonal injury

Andrew G. Reaume, Jeffrey L. Elliott, Eric K. Hoffman et al. · Nature Genetics · 1996 · 1.3K citations

, , +17