Pharmacological enhancement of <i>KCC2</i> gene expression exerts therapeutic effects on human Rett syndrome neurons and <i>Mecp2</i> mutant mice

Xin Tang, Jesse Drotar, Keji Li, Cullen Clairmont, A. Sophie Brumm, Austin Sullins, Hao Wu, Jinhua Wang, Nathanael S. Gray, Mriganka Sur,

Science Translational Medicine · 2019 · 121 citations · 78 references

DOIFull text

Open access

Concepts

Abstract

mutant mice ameliorated disease-associated respiratory and locomotion phenotypes. The small-molecule compounds described in our study may have therapeutic effects not only in RTT but also in other neurological disorders involving dysregulation of KCC2.

References

78