Science · 2006 · 246 citations · 18 references
MedicineDevelopmental BiologyGeneticsBone MetabolismGene ExpressionMorphogenesisBone DevelopmentBone FormationBone GrowthBone TissueOsteogenesisSkeletal DevelopmentBone Extracellular Matrix MineralizationBone Mass AcquisitionOsteoblast Gene ExpressionProtein Expression LevelsRegulation By E3 Ubiquitin LigasesRunx2 Transcription FactorRunx2 Transcriptional RegulationRunx2-mediated Osteogenesis
Genetic mutations that disrupt osteoblast function can result in skeletal dysmorphogenesis or, more rarely, in increased postnatal bone formation. Here we show that Schnurri-3 (Shn3), a mammalian homolog of the Drosophila zinc finger adapter protein Shn, is an essential regulator of adult bone formation. Mice lacking Shn3 display adult-onset osteosclerosis with increased bone mass due to augmented osteoblast activity. Shn3 was found to control protein levels of Runx2, the principal transcriptional regulator of osteoblast differentiation, by promoting its degradation through recruitment of the E3 ubiquitin ligase WWP1 to Runx2. By this means, Runx2-mediated extracellular matrix mineralization was antagonized, revealing an essential role for Shn3 as a central regulator of postnatal bone mass.
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Osf2/Cbfa1: A Transcriptional Activator of Osteoblast Differentiation
Patricia Ducy, Rui Zhang, Valérie Geoffroy et al. · Cell · 1997 · 4.3K citations · Full text