Selective vulnerability and pruning of phasic motoneuron axons in motoneuron disease alleviated by CNTF

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An adverse property of a familial ALS-linked SOD1 mutation causes motor neuron disease characterized by vacuolar degeneration of mitochondria

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Amyotrophic lateral sclerosis is a distal axonopathy: evidence in mice and man

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ALS-Linked SOD1 Mutant G85R Mediates Damage to Astrocytes and Promotes Rapidly Progressive Disease with SOD1-Containing Inclusions

Lucie Bruijn, Mark W. Bêcher, Michael K. Lee et al. · Neuron · 1997 · 1.3K citations · Full text

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Axonopathy and Transport Deficits Early in the Pathogenesis of Alzheimer's Disease

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