Nature Medicine · 2002 · 203 citations · 38 references
Life SciencesCell BiologyMolecular BiologyGene ExpressionGene RegulationMolecular Cell BiologyCalcium SignalingCalcium Transport ProteinsCystic FibrosisFibrosisIntracellular Calcium SignalingMucociliary ClearanceCalcium PumpsCftr Gene MutationsCftr Protein FunctionCystic Fibrosis GeneticsCystic Fibrosis Transmembrane Conductance Regulator Trafficking
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Degradation of CFTR by the ubiquitin-proteasome pathway
Cristina L. Ward, Satoshi ŌMURA, Ron R. Kopito · Cell · 1995 · 1.3K citations · Full text
Altered chloride ion channel kinetics associated with the ΔF508 cystic fibrosis mutation
Wilfried Dalemans, Pascal Barbry, Guy Champigny et al. · Nature · 1991 · 700 citations