Concepedia

Properdin Deficiency

Properdin Deficiency is a rare X-linked primary immunodeficiency disorder characterized by the impaired stabilization of the alternative pathway C3 convertase due to deficient or dysfunctional properdin, leading to increased susceptibility to recurrent pyogenic infections, particularly Neisseria species.

136

Publications

7.4K

Citations

457

Authors

190

Institutions

Publications per year

2017–2026

9

Parents

Publications

136

THE PROPERDIN SYSTEM AND IMMUNITY

Louis Pillemer, Livia Blum, Irwin H. Lepow et al. · The Journal of Experimental Medicine · 1956 · 357 citations · Full text

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A new complement function: solubilization of antigen-antibody aggregates.

Gary W. Miller, Victor Nussenzweig · Proceedings of the National Academy of Sciences · 1975 · 300 citations · Full text

, , +13

QUANTITATIVE STUDIES OF PHAGOCYTOSIS

Thomas P. Stossel · The Journal of Cell Biology · 1973 · 208 citations · Full text

, , +13

THE PROPERDIN SYSTEM AND IMMUNITY

A. C. Wardlaw, Louis Pillemer · The Journal of Experimental Medicine · 1956 · 171 citations · Full text

, , +10

Assessment of Complement Deficiency in Patients with Meningococcal Disease in the Netherlands

C. A. P. Fijen, Ed J. Kuijper, Marie T. te Bulte et al. · Clinical Infectious Diseases · 1999 · 161 citations · Full text

, , +11

1–5 of 136

Authors

457

  1. AG
    Anders G. Sjöholm

    Lund University, Sweden

    12 publications · 547 citations

    12

    h-index

  2. CS
    Cordula Stover

    University of Leicester, United Kingdom

    12 publications · 370 citations

    12

    h-index

  3. LP
    Louis Pillemer

    Case Western Reserve University, United States

    12 publications · 1.1K citations

    11

    h-index

  4. EJ
    Ed J. Kuijper

    Leiden University Medical Center, Netherlands

    9 publications · 561 citations

    9

    h-index

  5. CA
    Chester A. Alper

    Harvard University, United States

    8 publications · 694 citations

    8

    h-index

1–5 of 457

Institutions

190

  1. Lund University

    Lund, Sweden

    13 h-index

    44 publications

    1.6K citations

  2. University of Leicester

    Leicester, United Kingdom

    12 h-index

    48 publications

    1.2K citations

  3. Case Western Reserve University

    Cleveland, United States

    11 h-index

    41 publications

    4.2K citations

  4. University of Amsterdam

    Amsterdam, The Netherlands

    8 h-index

    32 publications

    2.8K citations

  5. University of Pennsylvania

    Philadelphia, United States

    7 h-index

    25 publications

    1.5K citations

  6. Harvard University

    Cambridge, United States

    5 h-index

    13 publications

    1.1K citations

  7. Translational Therapeutics (United States)

    Arlington, United States

    5 h-index

    22 publications

    832 citations

  8. Dana-Farber/Boston Children's Cancer and Blood Disorders Center

    Boston, United States

    4 h-index

    14 publications

    932 citations

1–8 of 190

Venues

  1. The Journal of Immunology

    JI · 17 publications · 690 citations

    13

    h-index

  2. PubMed

    Repository · 12 publications · 740 citations

    12

    h-index

  3. The Journal of Experimental Medicine

    8 publications · 983 citations

    8

    h-index

  4. Clinical & Experimental Immunology

    CEI · 8 publications · 385 citations

    8

    h-index

  5. New England Journal of Medicine

    NEJM · 6 publications · 568 citations

    6

    h-index

1–5