Francesco Bruni

The GABA Transaminase, ABAT, Is Essential for Mitochondrial Nucleoside Metabolism

Arnaud Besse, Ping Chun Wu, Francesco Bruni et al. · Cell Metabolism · 2015 · 162 citations · Full text

Cellular Enzymology, Biochemistry, Mitochondrial Function +7

Defective i6A37 Modification of Mitochondrial and Cytosolic tRNAs Results from Pathogenic Mutations in TRIT1 and Its Substrate tRNA

John W. Yarham, Tek N. Lamichhane, Angela Pyle et al. · PLoS Genetics · 2014 · 134 citations · Full text

Systems Biology, Mitochondrial Biogenesis, Mitochondrial Function +15

Nuclear Respiratory Factor 2 Induces the Expression of Many but Not All Human Proteins Acting in Mitochondrial DNA Transcription and Replication

Francesco Bruni, Paola Loguercio Polosa, Maria Nicola Gadaleta et al. · Journal of Biological Chemistry · 2009 · 75 citations · Full text

Reductive Stress, Transcriptional Regulation, Systems Biology +12

A human mitochondrial poly(A) polymerase mutation reveals the complexities of post-transcriptional mitochondrial gene expression

William C. Wilson, Hue-Tran Hornig-Do, Francesco Bruni et al. · Human Molecular Genetics · 2014 · 74 citations · Full text

Polymerase Mutation, Mitochondrial Biogenesis, Mitochondrial Function +12

REXO2 Is an Oligoribonuclease Active in Human Mitochondria

Francesco Bruni, Pasqua Gramegna, Jorge M.A. Oliveira et al. · PLoS ONE · 2013 · 62 citations · Full text

Oligoribonuclease Active, Biochemistry, Mitochondrial Function +14