Concepedia

Energy Metabolism and Mitochondrial Superoxide Anion Production in Pre-symptomatic Striatal Neurons Derived from Human-Induced Pluripotent Stem Cells Expressing Mutant Huntingtin

James Hamilton, Tatiana Brustovetsky, Akshayalakshmi Sridhar, Yanling Pan, Theodore Cummins, Jason S. Meyer, Nickolay Brustovetsky

Molecular Neurobiology · 2019 · 24 citations · 42 references

DOI

Concepts

References

42

A novel gene containing a trinucleotide repeat that is expanded and unstable on Huntington's disease chromosomes

Marcy E. MacDonald · Cell · 1993 · 8.4K citations · Full text

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Exon 1 of the HD Gene with an Expanded CAG Repeat Is Sufficient to Cause a Progressive Neurological Phenotype in Transgenic Mice

Laura Mangiarini, Kirupa Sathasivam, Mary J. Seller et al. · Cell · 1996 · 3.1K citations · Full text

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Disease-Specific Induced Pluripotent Stem Cells

In‐Hyun Park, Natasha Arora, Hongguang Huo et al. · Cell · 2008 · 2.2K citations · Full text

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Selective striatal neuronal loss in a YAC128 mouse model of Huntington disease

Elizabeth Slow · Human Molecular Genetics · 2003 · 802 citations · Full text

, , +17

Human iPSC-Based Modeling of Late-Onset Disease via Progerin-Induced Aging

Justine D. Miller, Yosif Ganat, Sarah Kishinevsky et al. · Cell stem cell · 2013 · 768 citations · Full text

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