Correction of Ductal CFTR Activity Rescues Acinar Cell and Pancreatic and Salivary Gland Functions in Mouse Models of Autoimmune Disease

A CFTR Potentiator in Patients with Cystic Fibrosis and the <i>G551D</i> Mutation

Bonnie W. Ramsey, Jane C. Davies, Noel G. McElvaney et al. · New England Journal of Medicine · 2011 · 2.2K citations · Full text

Medicine, Molecular Biology, Molecular Genetics +8

A CFTR corrector (lumacaftor) and a CFTR potentiator (ivacaftor) for treatment of patients with cystic fibrosis who have a phe508del CFTR mutation: a phase 2 randomised controlled trial

Michael Boyle, Scott C. Bell, Michael W. Konstan et al. · The Lancet Respiratory Medicine · 2014 · 442 citations

Pharmacy, Molecular Genetics, Pharmacotherapy +11

Aberrant CFTR-dependent HCO-3 transport in mutations associated with cystic fibrosis

Joo Young Choi, Daniella Muallem, Kirill Kiselyov et al. · Nature · 2001 · 412 citations · Full text

Medicine, Genetics, Molecular Genetics +12

Subclassification of Autoimmune Pancreatitis

Vikram Deshpande, Rajib Gupta, Nisha I. Sainani et al. · The American Journal of Surgical Pathology · 2010 · 204 citations · Full text

Medicine, Pathology, Anatomic Pathology +16

Alcohol Disrupts Levels and Function of the Cystic Fibrosis Transmembrane Conductance Regulator to Promote Development of Pancreatitis

József Maléth, Anita Balázs, Petra Pallagi et al. · Gastroenterology · 2014 · 199 citations · Full text

Medicine, Pathobiology, Pharmacology +14