Concepedia

Assessment of clinical response to ivacaftor with lung clearance index in cystic fibrosis patients with a G551D- CFTR mutation and preserved spirometry: a randomised controlled trial

Jane C. Davies, Helen Sheridan, Nicholas Bell, Steve Cunningham, Stephanie D. Davis, J.S. Elborn, Carlos Milla, Timothy D. Starner, Daniel J. Weiner, Po‐Shun Lee,

The Lancet Respiratory Medicine · 2013 · 224 citations · 22 references

DOI

Concepts

References

22

A CFTR Potentiator in Patients with Cystic Fibrosis and the <i>G551D</i> Mutation

Bonnie W. Ramsey, Jane C. Davies, Noel G. McElvaney et al. · New England Journal of Medicine · 2011 · 2.2K citations · Full text

, , +8

Changes in the normal maximal expiratory flow-volume curve with growth and aging.

Ronald J. Knudson, M D Lebowitz, Catharine J. Holberg et al. · PubMed · 1983 · 1.9K citations

, , +17

Cystic Fibrosis

Steven M. Rowe, Stacey Miller, Eric J. Sorscher · New England Journal of Medicine · 2005 · 1.4K citations

, , +13

Rescue of CF airway epithelial cell function in vitro by a CFTR potentiator, VX-770

Fredrick Van Goor, Sabine Hadidaꝉ, Peter D. J. Grootenhuis et al. · Proceedings of the National Academy of Sciences · 2009 · 1.2K citations · Full text

, , +17

Effect of VX-770 in Persons with Cystic Fibrosis and the G551D- <i>CFTR</i> Mutation

Frank J. Accurso, Steven M. Rowe, John P. Clancy et al. · New England Journal of Medicine · 2010 · 802 citations · Full text

, , +12