Molecular and Cellular Biology · 2002 · 251 citations · 41 references
Life SciencesGeneticsOncologyCancer GeneticsDna RepairRadiobiologyBreast Cancer RadiobiologyCancer CytogeneticsCancer Genomic InstabilityRadiation TherapyBrca2 DeficiencyBrca2 FunctionCell-cycle Checkpoint RegulationDna Interstrand CrosslinksGenome Instability In CancerHomologous Recombination RepairMutation SpectrumRadiation-induced Genomic Instability
We show here that the radiosensitive Chinese hamster cell mutant (V-C8) of group XRCC11 is defective in the breast cancer susceptibility gene Brca2. The very complex phenotype of V-C8 cells is complemented by a single human chromosome 13 providing the BRCA2 gene, as well as by the murine Brca2 gene. The Brca2 deficiency in V-C8 cells causes hypersensitivity to various DNA-damaging agents with an extreme sensitivity toward interstrand DNA cross-linking agents. Furthermore, V-C8 cells show radioresistant DNA synthesis after ionizing radiation, suggesting that Brca2 deficiency affects cell cycle checkpoint regulation. In addition, V-C8 cells display tremendous chromosomal instability and a high frequency of abnormal centrosomes. The mutation spectrum at the hprt locus showed that the majority of spontaneous mutations in V-C8 cells are deletions, in contrast to wild-type V79 cells. A mechanistic explanation for the genome instability phenotype of Brca2-deficient cells is provided by the observation that the nuclear localization of the central DNA repair protein in homologous recombination, Rad51, is reduced in V-C8 cells.
41
Embryonic lethality and radiation hypersensitivity mediated by Rad51 in mice lacking Brca2
Shyam K. Sharan, Masami Morimatsu, Urs Albrecht et al. · Nature · 1997 · 1.1K citations · Full text
The complete BRCA2 gene and mutations in chromosome 13q-linked kindreds
Sean V. Tavtigian, Jacques Simard, Johanna M. Rommens et al. · Nature Genetics · 1996 · 844 citations