PRIMARY HYPEROXALURIA TYPE 1: IMPROVED OUTCOME WITH TIMELY LIVER TRANSPLANTATION: A SINGLE-CENTER REPORT OF 36 CHILDREN

Abstract

Our decade-long experience with children with PH-1 supports strategies for early diagnosis and timely liver transplantation. Preemptive isolated liver transplantation should be considered in children who develop the disease during infancy or in those with slowly progressive disease when significant symptoms develop. Combined liver-kidney transplantation is suggested for children with end-stage renal disease.