Science · 2010 · 1.8K citations · 24 references
Life SciencesNeurobiologyNeuroscienceMolecular NeurobiologyMolecular NeuroscienceNeurodegenerationNeurodegeneration MechanismsNeurodegenerative DiseasesNeurodegenerative DisordersNeurotransmissionNeurotransmitter ReleaseSynaptic TransmissionIsolationMembrane Snare ComplexesNeurodegeneration PathogenesisPathogenic EffectsPresynaptic DysfunctionPresynaptic Terminal OrganizationSnare Complex DisassemblySnare Proteins
Presynaptic terminals repeatedly release neurotransmitters, requiring continuous SNARE‑complex assembly, yet the role of presynaptic proteins such as α‑synuclein in this process remains poorly understood. We demonstrate that α‑synuclein directly binds VAMP2 and acts as a nonclassical chaperone to promote SNARE‑complex assembly, and that synuclein‑deficient mice exhibit reduced assembly, age‑dependent neurological deficits, and premature death, indicating a role for synucleins in sustaining presynaptic function during aging.
Presynaptic nerve terminals release neurotransmitters repeatedly, often at high frequency, and in relative isolation from neuronal cell bodies. Repeated release requires cycles of soluble N-ethylmaleimide-sensitive factor attachment protein receptor (SNARE)-complex assembly and disassembly, with continuous generation of reactive SNARE-protein intermediates. Although many forms of neurodegeneration initiate presynaptically, only few pathogenic mechanisms are known, and the functions of presynaptic proteins linked to neurodegeneration, such as α-synuclein, remain unclear. Here, we show that maintenance of continuous presynaptic SNARE-complex assembly required a nonclassical chaperone activity mediated by synucleins. Specifically, α-synuclein directly bound to the SNARE-protein synaptobrevin-2/vesicle-associated membrane protein 2 (VAMP2) and promoted SNARE-complex assembly. Moreover, triple-knockout mice lacking synucleins developed age-dependent neurological impairments, exhibited decreased SNARE-complex assembly, and died prematurely. Thus, synucleins may function to sustain normal SNARE-complex assembly in a presynaptic terminal during aging.
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