Clinical presentation and pre-mortem diagnosis of variant Creutzfeldt-Jakob disease associated with blood transfusion: a case report

S. Wroe, Suvankar Pal, Durrenajaf Siddique, +8

The Lancet

Creutzfeldt-jakob DiseaseTransfusion MedicineHematologyPathologyNeurology +5

Molecular classification of sporadic Creutzfeldt–Jakob disease

Andrew F. Hill, Susan Joiner, Jonathan D. F. Wadsworth, +5

Brain

Strain-specific prion-protein conformation determined by metal ions

Jonathan D. F. Wadsworth, Andrew F. Hill, Susan Joiner, +3

Nature Cell Biology

Metal IonsBiochemistryProtein FoldingNatural SciencesMedicine +5

Species-barrier-independent prion replication in apparently resistant species

Andrew F. Hill, Susan Joiner, Jackie Linehan, +3

Proceedings of the National Academy of Sciences

Human Prion Protein with Valine 129 Prevents Expression of Variant CJD Phenotype

Jonathan D. F. Wadsworth, Emmanuel A. Asante, Melanie Desbruslais, +9

Science

A Novel Prion Disease Associated with Diarrhea and Autonomic Neuropathy

Simon Mead, Sonia Gandhi, Jon Beck, +22

New England Journal of Medicine

2.7 Å cryo-EM structure of ex vivo RML prion fibrils

Szymon W. Manka, Wenjuan Zhang, Adam Wenborn, +5

Nature Communications

Single Prp MonomerCreutzfeldt-jakob DiseaseBiochemistryProtein AssemblyProtein Folding +12

Distinct glycoform ratios of protease resistant prion protein associated with PRNP point mutations

Andrew F. Hill, Susan Joiner, Jonathan Beck, +5

Brain

Kuru prions and sporadic Creutzfeldt–Jakob disease prions have equivalent transmission properties in transgenic and wild-type mice

Jonathan D. F. Wadsworth, Susan Joiner, Jacqueline M. Linehan, +9

Proceedings of the National Academy of Sciences

Knockout MouseWild-type MiceMolecular NeuroscienceCreutzfeldt-jakob DiseaseGenetics +10

Molecular screening of sheep for bovine spongiform encephalopathy

Andrew F. Hill, Katie Sidle, Susan Joiner, +4

Neuroscience Letters

CaprineAnimal SciencePathogenesisVeterinary SciencePathology +3