Concepedia
Author
Jean Bastin
Also Known As
J BASTIN, J Bastin, J M Bastin, J. Bastin, JEAN BASTIN, Jean BASTIN, Jean Bastin, R Mcandrew, S. Mouillet-Richard, Sophie Mouillet-Richard
90
Publications
4K
Citations
33
H-Index
103
Concepts
All Affiliations
1
20
26
1.7K
2
13
14
980
3
91
4
36
5
17
×
All Concepts
48
3.4K
30
Fatty Acid Oxidation Enzyme Gene Expression Is Downregulated in the Failing Heart
Michael N. Sack, Toni A. Rader, Sonhee Park, +3
Circulation
1996
676
A gender-related defect in lipid metabolism and glucose homeostasis in peroxisome proliferator- activated receptor alpha- deficient mice.
Fatima Djouadi, Carla J. Weinheimer, Jeffrey E. Saffitz, +4
Journal of Clinical Investigation
GeneticsLipid PeroxidationGlucose HomeostasisCellular Lipid UtilizationPparalpha Target Genes +16
1998
405
Inhibition of mitophagy drives macrophage activation and antibacterial defense during sepsis
Danish Patoli, Franck Mignotte, Valérie Deckert, +24
MitophagyMicrobial PathogensInnate Immune SystemImmunologyImmune Regulation +21
2020
224
S6 Kinase Deletion Suppresses Muscle Growth Adaptations to Nutrient Availability by Activating AMP Kinase
Víctor Aguilar, Samira Alliouachene, Athanassia Sotiropoulos, +15
Cell Metabolism
Muscle PhysiologyMuscle FunctionMolecular PhysiologySignal TransductionSkeletal Muscle +10
2007
181
Activation of Peroxisome Proliferator-Activated Receptor Pathway Stimulates the Mitochondrial Respiratory Chain and Can Correct Deficiencies in Patients’ Cells Lacking Its Components
Jean Bastin, Flore Aubey, Agnès Rötig, +2
The Journal of Clinical Endocrinology & Metabolism
2008
138
Long-Term Follow-Up of Bezafibrate Treatment in Patients With the Myopathic Form of Carnitine Palmitoyltransferase 2 Deficiency
Jean‐Paul Bonnefont, Jean Bastin, Pascal Laforêt, +10
Clinical Pharmacology & Therapeutics
2010
123
Bezafibrate increases very-long-chain acyl-CoA dehydrogenase protein and mRNA expression in deficient fibroblasts and is a potential therapy for fatty acid oxidation disorders
Fatima Djouadi, Flore Aubey, Dimitri Schlemmer, +4
Human Molecular Genetics
2005
94
Genetic Basis for Correction of Very-Long-Chain Acyl–Coenzyme A Dehydrogenase Deficiency by Bezafibrate in Patient Fibroblasts: Toward a Genotype-Based Therapy
S. Gobin-Limballe, Fatima Djouadi, Flore Aubey, +10
The American Journal of Human Genetics
Genetic DiseasesGene TherapiesGenotype-based TherapyMendelian DisorderGenetic Disorder +10
74
Exposure to resveratrol triggers pharmacological correction of fatty acid utilization in human fatty acid oxidation-deficient fibroblasts
Jean Bastin, A. Lopes-Costa, Fatima Djouadi
Triggers Pharmacological CorrectionLipid PeroxidationVlcad DeficiencyPolyphenolicsOxidative Stress +18
2011
70
A Subset of Patients With Autism Spectrum Disorders Show a Distinctive Metabolic Profile by Dried Blood Spot Analyses
Rita Barone, Salvatore Alaimo, Marianna Messina, +2
Frontiers in Psychiatry
2018
64
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