Sabrina Noël

A Phase 3 Open-Label Study of Elexacaftor/Tezacaftor/Ivacaftor in Children 6 through 11 Years of Age with Cystic Fibrosis and at Least One <i>F508del</i> Allele

Edith T. Zemanick, Jennifer L. Taylor‐Cousar, Jane C. Davies et al. · American Journal of Respiratory and Critical Care Medicine · 2021 · 288 citations · Full text

Pharmacy, Pediatrics, Pharmacology +15

Reduced histone deacetylase 7 activity restores function to misfolded CFTR in cystic fibrosis

Darren M. Hutt, David Herman, Ana P. C. Rodrigues et al. · Nature Chemical Biology · 2009 · 250 citations · Full text

Life Sciences, Cell Biology, Molecular Biology +15

Efficacy and Safety of Elexacaftor/Tezacaftor/Ivacaftor in Children 6 Through 11 Years of Age with Cystic Fibrosis Heterozygous for <i>F508del</i> and a Minimal Function Mutation: A Phase 3b, Randomized, Placebo-controlled Study

Marcus Mall, Rossa Brugha, Silvia Gärtner et al. · American Journal of Respiratory and Critical Care Medicine · 2022 · 140 citations · Full text

Pharmacy, Pediatrics, Pharmacotherapy +15

Rescue of functional delF508‐CFTR channels in cystic fibrosis epithelial cells by the α‐glucosidase inhibitor miglustat

Caroline Norez, Sabrina Noël, Martina Wilke et al. · FEBS Letters · 2006 · 127 citations

Life Sciences, Molecular Biology, Molecular Genetics +10

Airway surface liquid acidification initiates host defense abnormalities in Cystic Fibrosis

Juliette Simonin, Emmanuelle Bille, Gilles Crambert et al. · Scientific Reports · 2019 · 85 citations · Full text

Life Sciences, Microbiology, Innate Immunity +16