V. Decostre - Concepedia

Author

V. Decostre

Also Known As

A. Canal, Decostre, V., Li, Juan, Nicolas Champtiaux, V Decostre, V. Decostre, Valerie Decostre, Valérie Decostre, Valérie Decostre, Valérie Decostre (115607)

Publications

1.8K

Citations

H-Index

Concepts

All Affiliations

Institut de Myologie Sorbonne Université Inserm Assistance Publique – Hôpitaux de Paris Centre de Recherche en Myologie

About

V. Decostre is an author at Institut de Myologie specializing in medicine, health sciences, and applied physiology.

Top Concepts

#	Concept	H-Index	Publications	Citations
1	Medicine	12	12	724
2	Health Sciences	10	10	311
3	Engineering	1	1	16
4	Natural Sciences	1	1	75
5	Social Sciences	1	1	28

V. Decostre

Publications

1.5K

Citations

H-Index

Page 1

	Year	Citations
Activation of MAPK pathways links LMNA mutations to cardiomyopathy in Emery-Dreifuss muscular dystrophy Antoine Muchir, Paul Pavlidis, V. Decostre, Journal of Clinical Investigation Cardiac MuscleCardiomyopathyLmna MutationsSignal TransductionMolecular Physiology	2007	298
Lamin A/C–mediated neuromuscular junction defects in Emery-Dreifuss muscular dystrophy Alexandre Méjat, V. Decostre, Juan Li, The Journal of Cell Biology	2009	116
Molecular, Physiological, and Motor Performance Defects in DMSXL Mice Carrying >1,000 CTG Repeats from the Human DM1 Locus Aline Huguet, Fadia Medja, Annie Nicole, PLoS Genetics	2012	113
Upper Limb Strength and Function Changes during a One-Year Follow-Up in Non-Ambulant Patients with Duchenne Muscular Dystrophy: An Observational Multicenter Trial A. Seferian, A. Moraux, M. Annoussamy, PLoS ONE	2015	75
DelK32-lamin A/C has abnormal location and induces incomplete tissue maturation and severe metabolic defects leading to premature death A. Bertrand, Laure Renou, Aurélie Papadopoulos, Human Molecular Genetics Molecular RegulationGeneticsApoptosisCell DeathPathology	2011	75
Longitudinal functional and NMR assessment of upper limbs in Duchenne muscular dystrophy Jean‐Yves Hogrel, Claire Wary, A. Moraux, Neurology	2016	74
Upper Limb Evaluation and One-Year Follow Up of Non-Ambulant Patients with Spinal Muscular Atrophy: An Observational Multicenter Trial A. Seferian, A. Moraux, Aurélie Canal, PLoS ONE Observational Multicenter TrialMuscle FunctionUpper ExtremityOrthopaedic SurgeryKinesiology	2015	64
Heterozygous LmnadelK32 mice develop dilated cardiomyopathy through a combined pathomechanism of haploinsufficiency and peptide toxicity Marie‐Elodie Cattin, A. Bertrand, Saskia Schlossarek, Human Molecular Genetics	2013	63
Stature is an essential predictor of muscle strength in children Jean‐Yves Hogrel, V. Decostre, Corinne Alberti, BMC Musculoskeletal Disorders	2012	57
Quadriceps strength is a sensitive marker of disease progression in sporadic inclusion body myositis Yves Allenbach, Olivier Benvéniste, V. Decostre, Neuromuscular Disorders Sensitive MarkerQuadriceps StrengthDisease ProgressionMedicineImmunology	2012	50

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