Steven U. Walkley - Concepedia

Author

Steven U. Walkley

Albert Einstein College of Medicine ORCID

Also Known As

S U Walkley, S. U. Walkley, S. Walkley, S.U. Walkley, STEVEN U. WALKLEY, Steven U Walkley, Steven U. Walkley, Steven Walkley, Steven U. Walkley

157

Publications

8.5K

Citations

H-Index

106

Concepts

All Affiliations

Albert Einstein College of Medicine John F. Kennedy Center for the Performing Arts Washington University in St. Louis University of Pennsylvania National Institutes of Health

About

Steven U. Walkley is an author at Albert Einstein College of Medicine specializing in medicine, neurology, and neuropathology.

Top Concepts

#	Concept	H-Index	Publications	Citations
1	Medicine	31	51	3.9K
2	Social Sciences	11	13	921
3	Natural Sciences	5	5	857
4	Health Sciences	2	2	103
5	Education	1	1	28

Steven U. Walkley

Publications

6.5K

Citations

H-Index

Page 1

	Year	Citations
Chronic Cyclodextrin Treatment of Murine Niemann-Pick C Disease Ameliorates Neuronal Cholesterol and Glycosphingolipid Storage and Disease Progression Cristin Davidson, Nafeeza Ali, Matthew C. Micsenyi, PLoS ONE	2009	449
Genetic evidence for nonredundant functional cooperativity between NPC1 and NPC2 in lipid transport David E. Sleat, Jennifer A. Wiseman, Mukarram El-Banna, Proceedings of the National Academy of Sciences Proteinlipid InteractionMolecular BiologyLipid MovementCellular PhysiologyMembrane Transport	2004	369
Critical role for glycosphingolipids in Niemann-Pick disease type C Mark Zervas, Kyra L Somers, Mary Anna Thrall, Current Biology Autoimmune DiseaseDisease MechanismG Protein-coupled ReceptorCritical RolePathogenesis	2001	330
Intrathecal 2-hydroxypropyl-β-cyclodextrin decreases neurological disease progression in Niemann-Pick disease, type C1: a non-randomised, open-label, phase 1–2 trial Daniel S. Ory, Elizabeth A. Ottinger, Nicole Y. Farhat, The Lancet Neurodegenerative DiseasesNeurobiology Of DiseaseClinical TherapeuticNiemann-pick DiseasePharmacology	2017	316
Neurons in Niemann-Pick Disease Type C Accumulate Gangliosides as Well as Unesterified Cholesterol and Undergo Dendritic and Axonal Alterations Mark Zervas, Kostantin Dobrenis, Steven U. Walkley Journal of Neuropathology & Experimental Neurology PathologyAxonal AlterationsCellular PhysiologySocial SciencesNeuroinflammation	2001	266
Intracisternal cyclodextrin prevents cerebellar dysfunction and Purkinje cell death in feline Niemann-Pick type C1 disease Charles H. Vite, Jessica Bagel, Gary P. Swain, Science Translational Medicine	2015	207
Differential subcellular localization of cholesterol, gangliosides, and glycosaminoglycans in murine models of mucopolysaccharide storage disorders Robert McGlynn, Kostantin Dobrenis, Steven U. Walkley The Journal of Comparative Neurology Free CholesterolGlycobiologyPathologyExperimental PathologyLipid Movement	2004	198
A mouse model for mucopolysaccharidosis type III A (Sanfilippo syndrome) Mantu Bhaumik, Vivienne Muller, Tina Rozaklis, Glycobiology	1999	187
Bone marrow transplantation corrects the enzyme defect in neurons of the central nervous system in a lysosomal storage disease. Steven U. Walkley, M. A. Thrall, Kostantin Dobrenis, Proceedings of the National Academy of Sciences Social SciencesNeuroregenerationEnzyme DefectBone Marrow FailureNeurology	1994	186
Pregnane X receptor (PXR) activation: A mechanism for neuroprotection in a mouse model of Niemann–Pick C disease S. Joshua Langmade, Sarah E. Gale, Andrey Frolov, Proceedings of the National Academy of Sciences Niemann–pick C DiseaseImmunologyCell DeathNeuroinflammationExperimental Neuropathology	2006	166

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