Tania Tiepolo

Autophagy is defective in collagen VI muscular dystrophies, and its reactivation rescues myofiber degeneration

Paolo Grumati, Luisa Coletto, Patrizia Sabatelli et al. · Nature Medicine · 2010 · 519 citations · Full text

Cell Autophagy, Mitophagy, Developmental Biology +9

Cyclosporin A corrects mitochondrial dysfunction and muscle apoptosis in patients with collagen VI myopathies

Luciano Merlini, Alessia Angelin, Tania Tiepolo et al. · Proceedings of the National Academy of Sciences · 2008 · 201 citations · Full text

Cell Death, Pathology, Cyclosporin A +17

Mitochondrial dysfunction in the pathogenesis of Ullrich congenital muscular dystrophy and prospective therapy with cyclosporins

Alessia Angelin, Tania Tiepolo, Patrizia Sabatelli et al. · Proceedings of the National Academy of Sciences · 2007 · 184 citations · Full text

Mitochondrial Myopathy, Mechanobiology, Muscle Pathology +13

Genetic ablation of cyclophilin D rescues mitochondrial defects and prevents muscle apoptosis in collagen VI myopathic mice

Elena Palma, Tania Tiepolo, Alessia Angelin et al. · Human Molecular Genetics · 2009 · 128 citations · Full text

Mitochondrial Dysfunction, Apoptosis, Pathology +18

The cyclophilin inhibitor Debio 025 normalizes mitochondrial function, muscle apoptosis and ultrastructural defects in<i>Col6a1</i>^−/−myopathic mice

Tania Tiepolo, Alessia Angelin, Elena Palma et al. · British Journal of Pharmacology · 2009 · 117 citations · Full text