Concepedia

Author

Irene Sambri

Telethon Institute Of Genetics And MedicineORCID

Also Known As

Irene Sambri, Irene Sambri (333693), Sambri, Irene

21

Publications

688

Citations

12

H-Index

20

Concepts

All Affiliations

Telethon Institute Of Genetics And MedicineFederico II University HospitalUniversity of Campania "Luigi Vanvitelli"National Research CouncilUniversity of Naples Federico II
IS

About

Irene Sambri is an author at Telethon Institute Of Genetics And Medicine specializing in neurobiology of disease, medicine, and cellular neuroscience.

Top Concepts

#ConceptH-IndexPublicationsCitations

1

Medicine

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2

Social Sciences

1

1

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3

Cell Biology

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38

4

Neurology

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38

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Neuroscience

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38

Irene Sambri

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10

Publications

494

Citations

10

H-Index

YearCitations

A highly secreted sulphamidase engineered to cross the blood‐brain barrier corrects brain lesions of mice with mucopolysaccharidoses type IIIA

Nicolina Cristina Sorrentino, Luca D’Orsi, Irene Sambri,

EMBO Molecular Medicine

2013

108

Lysosomal dysfunction disrupts presynaptic maintenance and restoration of presynaptic function prevents neurodegeneration in lysosomal storage diseases

Irene Sambri, Rosa D’Alessio, Yulia Ezhova,

EMBO Molecular Medicine

2016

78

Protein Isoaspartate Methyltransferase Prevents Apoptosis Induced by Oxidative Stress in Endothelial Cells: Role of Bcl-Xl Deamidation and Methylation

Amelia Cimmino, Rosanna Capasso, Muller Fabbri,

PLoS ONE

2008

72

m-AAA and i-AAA complexes coordinate to regulate OMA1, the stress-activated supervisor of mitochondrial dynamics

Francesco Consolato, Francesca Maltecca, Susanna Tulli,

Journal of Cell Science

2018

56

Impaired flickering of the permeability transition pore causes SPG7 spastic paraplegia

Irene Sambri, Filomena Massa, Francesca Gullo,

EBioMedicine

2020

54

The Amyloid Inhibitor CLR01 Relieves Autophagy and Ameliorates Neuropathology in a Severe Lysosomal Storage Disease

Antonio Monaco, Veronica Maffia, Nicolina Cristina Sorrentino,

Molecular Therapy

2020

38

Homocysteinylated Albumin Promotes Increased Monocyte-Endothelial Cell Adhesion and Up-Regulation of MCP1, Hsp60 and ADAM17

Rosanna Capasso, Irene Sambri, Amelia Cimmino,

PLoS ONE

2012

32

The SGLT2 inhibitor dapagliflozin improves kidney function in glycogen storage disease XI

Francesco Trepiccione, Anna Iervolino, Mariavittoria D’Acierno,

Science Translational Medicine

2023

23

RagD auto-activating mutations impair MiT/TFE activity in kidney tubulopathy and cardiomyopathy syndrome

Irene Sambri, Marco Ferniani, Giulia Campostrini,

Nature Communications

2023

18

The MicroRNA 15a/16–1 Cluster Down-regulates Protein Repair Isoaspartyl Methyltransferase in Hepatoma Cells

Irene Sambri, Rosanna Capasso, Piero Pucci,

Journal of Biological Chemistry

2011

15

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