Concepedia
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Publications
4
Citations
115
H-Index
Active since
2018
Affiliations
University Hospital Cologne(Current)
University of Cologne
Cologne Excellence Cluster on Cellular Stress Responses in Aging Associated Diseases
Maximilian Paul Thelen is an author at University Hospital Cologne specializing in neuropathology, neurogenetics, and medicine.
Top concepts
GeneticsMedicineNeurologyNeuroscienceNeurogeneticsNeuropathologySocial SciencesMolecular NeuroscienceNeurobiology Of Disease
Publications per year
2018–2020
Mitochondrial defects in the respiratory complex I contribute to impaired translational initiation via ROS and energy homeostasis in SMA motor neurons
Maximilian Paul Thelen, Brunhilde Wirth, Min Jeong Kye · Acta Neuropathologica Communications · 2020 · 44 citations · Full text
Neuronal activity regulates DROSHA via autophagy in spinal muscular atrophy
Inês do Carmo G. Gonçalves, Johanna Brecht, Maximilian Paul Thelen et al. · Scientific Reports · 2018 · 26 citations · Full text
Muscle regulates mTOR dependent axonal local translation in motor neurons via CTRP3 secretion: implications for a neuromuscular disorder, spinal muscular atrophy
Wiebke A. Rehorst, Maximilian Paul Thelen, Hendrik Nolte et al. · Acta Neuropathologica Communications · 2019 · 25 citations · Full text
De Novo and Inherited Variants in GBF1 are Associated with Axonal Neuropathy Caused by Golgi Fragmentation
Natalia Mendoza-Ferreira, Mert Karakaya, Nur Cengiz et al. · The American Journal of Human Genetics · 2020 · 20 citations · Full text
Molecular Neuroscience, Neurobiology Of Disease, De Novo +11
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