Valeska Lizzi Lagranha

Clinical and biochemical study of 29 Brazilian patients with metachromatic leukodystrophy

Osvaldo Artigalás, Valeska Lizzi Lagranha, Maria Luiza Saraiva Pereira et al. · Journal of Inherited Metabolic Disease · 2010 · 27 citations

Medicine, Hematology, Pathology +4

In vivo experimental evidence that the major metabolites accumulating in 3-hydroxy-3-methylglutaryl-CoA lyase deficiency induce oxidative stress in striatum of developing rats: A potential pathophysiological mechanism of striatal damage in this disorder

Carolina Gonçalves Fernandes, Mateus Struecker da Rosa, Bianca Seminotti et al. · Molecular Genetics and Metabolism · 2013 · 27 citations

Life Sciences, Neurobiology, Neuroscience +17

Increased Glutamate Receptor and Transporter Expression in the Cerebral Cortex and Striatum of Gcdh-/- Mice: Possible Implications for the Neuropathology of Glutaric Acidemia Type I

Valeska Lizzi Lagranha, Úrsula da Silveira Matte, Talita Giacomet de Carvalho et al. · PLoS ONE · 2014 · 23 citations · Full text

Life Sciences, Neurobiology, Neuroscience +17

In vitro correction of ARSA deficiency in human skin fibroblasts from Metachromatic Leukodystrophy patients after treatment with microencapsulated recombinant cells

Valeska Lizzi Lagranha, Guilherme Baldo, Talita Giacomet de Carvalho et al. · Metabolic Brain Disease · 2008 · 23 citations

Medicine, Dermatology, Immunology +6

Effects of Cryopreservation and Hypothermic Storage on Cell Viability and Enzyme Activity in Recombinant Encapsulated Cells Overexpressing Alpha‐L‐Iduronidase

Fabiana Quoos Mayer, Guilherme Baldo, Talita Giacomet de Carvalho et al. · Artificial Organs · 2010 · 20 citations

Life Sciences, Biochemistry, Cell Biology +13