Monica Benini

E3 Ligase RNF126 Directly Ubiquitinates Frataxin, Promoting Its Degradation: Identification of a Potential Therapeutic Target for Friedreich Ataxia

Monica Benini, Silvia Fortuni, Ivano Condò et al. · Cell Reports · 2017 · 42 citations · Full text

Highly specific ubiquitin-competing molecules effectively promote frataxin accumulation and partially rescue the aconitase defect in Friedreich ataxia cells

Alessandra Rufini, Francesca Cavallo, Ivano Condò et al. · Neurobiology of Disease · 2014 · 33 citations · Full text

Drug repositioning screening identifies etravirine as a potential therapeutic for friedreich's ataxia

Giulia Alfedi, Riccardo Luffarelli, Ivano Condò et al. · Movement Disorders · 2019 · 33 citations

Frataxin deficiency in Friedreich’s ataxia is associated with reduced levels of HAX-1, a regulator of cardiomyocyte death and survival

Francesca Tiano, Francesca Amati, Fabio Cherubini et al. · Human Molecular Genetics · 2020 · 11 citations · Full text

Biophysical characterisation of the recombinant human frataxin precursor

Ignacio Hugo Castro, Alejandro Ferrari, María Georgina Herrera et al. · FEBS Open Bio · 2018 · 10 citations · Full text