Chordoid Sarcoma

Abstract

Four cases of a tumor histologically resembling chordoma but arising in soft parts of the extremities are presented, with clinical, radiographic, histologic, and histochemical features. In accord with the suggestion of Stewart, this rare, distinctive, malignant neoplasm has been designated “chordoid tumor” or “chordoid sarcoma.” Based on the results of treatment and clinical behavior in these cases en bloc excision or amputation appears to be the method of choice for therapy.