Journal of Biological Chemistry · 2020 · 25 citations · 52 references
Life SciencesBiologyGeneticsCellular MetabolismMetabolismMitochondrial BiologyIron MetabolismIron TransportMitochondrial BiochemistryMitochondrial BioenergeticsMitochondrial DysfunctionMitochondrial PhysiologyCardiolipin InvolvementCellular BioenergeticsFerroportin FunctionFerroportin Iron ExportIron Homeostasis DisruptionIron Homeostasis RegulationMitochondrial Iron ImportMitochondrial Iron Metabolism
Δ cells exhibited decreased processing of the Yfh1 precursor upon import, which likely contributes to the iron homeostasis defects. Implications for understanding the pathogenesis of BTHS are discussed.
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The iron exporter ferroportin/Slc40a1 is essential for iron homeostasis
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