F1000Research · 2019 · 53 citations · 28 references
MedicineDermatologyImmunologyImmunopathologyInflammationInnate ImmunityCytokine BiologyCytokine-mediated PathologyInflammatory DermatosesInflammatory Skin DiseasesInflammatory Skin DisordersNeutrophil BiologyAnti-neutrophil Cytoplasmic AntibodiesBiologic Therapy ManagementHomeostatic CytokinesNeutrophilic Dermatoses In AutoinflammationNeutrophilic Dermatoses In InfectionNeutrophilic InfiltratesPyoderma Gangrenosum
Pyoderma Gangrenosum (PG) is a rare neutrophilic dermatosis with multiple different clinical presentations and associated comorbidities. PG has historically been a challenging disorder to diagnose, leading to the development of new diagnostic criteria rather than the traditional approach of a diagnosis of exclusion. The pathophysiology is thought to involve both innate and adaptive immune system dysregulation, neutrophilic abnormalities, environmental, and genetic factors. As of today, no gold standard therapy exists for the treatment of PG, and the literature is restricted to mainly case reports, case series, and 2 small randomized clinical trials. Topical, systemic, and biologic therapy, as well as adequate analgesia and proper wound care all play a role in the management of PG. Recent studies have identified additional cytokines and signalling cascades thought to be involved in the pathogenesis of PG, ultimately leading to the development of new targeted therapies. This review will focus on recent advances in the pathophysiology, clinical presentation and associated comorbidities, diagnosis, and management of PG.
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Diagnostic Criteria of Ulcerative Pyoderma Gangrenosum
Emanual Maverakis, Chelsea Ma, Kanade Shinkai et al. · JAMA Dermatology · 2018 · 432 citations · Full text
Angelo Valerio Marzano, Daniele Fanoni, Emiliano Antiga et al. · Clinical & Experimental Immunology · 2014 · 239 citations · Full text
Medicine, Dermatology, Immunology +17