Oxford Medical Case Reports · 2019 · 13 citations · 5 references
Life SciencesImmunologyPathologyAnatomic PathologyAutoimmunityClinical ImmunologyAutoimmune Disease PathologyAutoimmune DiseasesClinical ManifestationsPleural DiseaseSystemic Autoimmune DiseaseSystemic Lupus ErythematosusLiver Biopsy HistopathologyLiver Biopsy InterpretationMalignant Pleural EffusionMeige DiseasePleural Effusion EvaluationSystemic Lupus Erythematosus AssociationsSystemic Lupus Erythematosus Diagnostics
Here we report a case of a patient with systemic lupus erythematosus presenting with pseudo-pseudo Meigs' syndrome (PPMS): a triad of pleural effusion, ascites and raised CA-125. There have only been nine other cases reported in the literature. To our knowledge, this is the first to have an oesophago-gastro-duodenoscopy and liver biopsy as part of the diagnostic work up. Its mechanism of action is not yet fully understood but PPMS is a treatable condition that is responsive to immunosuppression. It is therefore important to consider it in patients presenting like this, where alternative diagnoses, including malignancy, have been ruled out.
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