Concepedia

The addition of ketone bodies alleviates mitochondrial dysfunction by restoring complex I assembly in a MELAS cellular model

Samuel Frey, Guillaume Geffroy, Valérie Desquiret‐Dumas, Naïg Guéguen, Céline Bris, Sophie Belal, Patrizia Amati‐Bonneau, Arnaud Chevrollier, Magalie Barth, Daniel Henrion,

Biochimica et Biophysica Acta (BBA) - Molecular Basis of Disease · 2016 · 61 citations · 25 references

DOI

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References

25

A mutation in the tRNALeu(UUR) gene associated with the MELAS subgroup of mitochondrial encephalomyopathies

Yu‐ichi Goto, Ikuya Nonaka, Satoshi Horai · Nature · 1990 · 2.1K citations

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Mitochondrial myopathy, encephalopathy, lactic acidosis, and strokelike episodes: A distinctive clinical syndrome

Steven G. Pavlakis, Peter C. Phillips∥, Salvatore DiMauro et al. · Annals of Neurology · 1984 · 1.2K citations

Ketones inhibit mitochondrial production of reactive oxygen species production following glutamate excitotoxicity by increasing NADH oxidation

M. Maalouf, Patrick G. Sullivan, Lydia J. Davis et al. · Neuroscience · 2007 · 461 citations · Full text

, , +10

The Ketogenic Diet as a Treatment Paradigm for Diverse Neurological Disorders

Carl E. Stafstrom, Jong M. Rho · Frontiers in Pharmacology · 2012 · 436 citations · Full text

Functional Modules and Structural Basis of Conformational Coupling in Mitochondrial Complex I

Carola Hunte, Volker Zickermann, Ulrich Brandt · Science · 2010 · 368 citations

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