Prolonged survival in hydranencephaly: a case report.

Abstract

Individuals with hydranencephaly, a congenital deformity resulting in a virtual absence of cerebral hemispheres, generally do not survive past infancy. Two published cases report survival past the age of 10. We report the oldest known survivor at 20 years, 6 months and compare the behavioral and anatomical characteristics of these three cases. Finally, this condition is discussed in regards to the concept and implications of minimally conscious state (MCS).