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Brain Stem MRI Signal Abnormalities in CADASIL

Hugues Chabriat, Ridha Mrissa, C.D.P. Levy, Katayoun Vahedi, H. Taillia, M T Iba-Zizen, Anne Joutel, Elisabeth Tournier‐Lasserve, M.G. Bousser

Stroke · 1999 · 91 citations · 17 references

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Abstract

Brain stem signal abnormalities observed in CADASIL are found in regions irrigated only by perforating arteries. These results support parallel observations made for CADASIL-associated signal abnormalities in the cerebral hemispheres and emphasize the importance of the angioarchitecture of the cerebral vasculature to explain why a condition characterized by a systemic vessel wall pathology is manifested only as a brain disease.

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