Journal of Lipid Research · 2003 · 115 citations · 50 references
Life SciencesBiochemistryGeneticsLipid BiochemistryMetabolic RegulationMetabolismBile Acid MetabolismCholesterol BiosynthesisCholesterol MetabolismLipid HomeostasisLipid MetabolismLipoprotein MetabolismBile Acid Homeostasis In DiseaseBile Acid Synthesis DefectsBile Acid Synthesis EnzymesBile Acid Synthesis RegulationCholesterol 7 Alpha-hydroxylase RegulationHigh-density Lipoprotein MetabolismLipid Metabolism EffectsLipoprotein Metabolism Regulation
Cholesterol 7alpha-hydroxylase, a rate-limiting enzyme for bile acid synthesis, has been implicated in genetic susceptibility to atherosclerosis. The gene, CYP7A1, encoding a protein with this activity, is expressed normally only in hepatocytes and is highly regulated. Our cyp7A1 gene knockout mouse colony, as young adults on a chow diet, is hypercholesterolemic. These mice were characterized extensively to understand how cyp7A1 affects lipid and bile acid homeostasis in different tissue compartments and whether gender plays a modifying role. Both male and female cyp7A1-deficient mice had decreased hepatic LDL receptors, unchanged hepatic cholesterol synthesis, increased intestinal cholesterol synthesis and bile acid transporters, and decreased fecal bile acids but increased fecal sterols. In females, cyp7A1 deficiency also caused changes in hepatic fatty acid metabolism, decreased hepatic canalicular bile acid transporter, Bsep, and gallbladder bile composition altered to a lithogenic profile. Taken together, the data suggest that cyp7A1 deficiency results in a proatherogenic phenotype in both genders and leads to a prolithogenic phenotype in females.
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