Concepedia

An ALS-associated mutation affecting TDP-43 enhances protein aggregation, fibril formation and neurotoxicity

Weirui Guo, Yanbo Chen, Xiaohong Zhou, Amar N. Kar, Payal Ray, Xiaoping Chen, Elizabeth J. Rao, Mengxue Yang, Haihong Ye, Li Zhu,

Nature Structural & Molecular Biology · 2011 · 311 citations · 43 references

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43

Ubiquitinated TDP-43 in Frontotemporal Lobar Degeneration and Amyotrophic Lateral Sclerosis

Manuela Neumann, Deepak M. Sampathu, Linda K. Kwong et al. · Science · 2006 · 6.6K citations

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ExPASy: the proteomics server for in-depth protein knowledge and analysis

Elisabeth Gasteiger · Nucleic Acids Research · 2003 · 5.7K citations · Full text

, , +17

TDP-43 is a component of ubiquitin-positive tau-negative inclusions in frontotemporal lobar degeneration and amyotrophic lateral sclerosis

Tetsuaki Arai, Masato Hasegawa, Haruhiko Akiyama et al. · Biochemical and Biophysical Research Communications · 2006 · 2.8K citations

, , +11

TDP-43 Mutations in Familial and Sporadic Amyotrophic Lateral Sclerosis

Jemeen Sreedharan, Ian P. Blair, Vineeta B. Tripathi et al. · Science · 2008 · 2.6K citations · Full text

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Mutations in the <i>FUS/TLS</i> Gene on Chromosome 16 Cause Familial Amyotrophic Lateral Sclerosis

Thomas J. Kwiatkowski, Daryl A. Bosco, Aurélie Leclerc et al. · Science · 2009 · 2.6K citations

, , +14