Concepedia

ANCA-associated vasculitis is linked to carriage of the Z allele of α1 antitrypsin and its polymers

Hannah L. Morris, M. D. Morgan, Alice M. Wood, Stuart W. Smith, Ugo Ekeowa, Kristine Herrmann, Julia U. Holle, Loı̈c Guillevin, David A. Lomas, Charles D. Pusey,

Annals of the Rheumatic Diseases · 2011 · 69 citations · 27 references

DOI

References

27

The mechanism of Z α1-antitrypsin accumulation in the liver

David A. Lomas, Dyfed LI-Evans, J.T. Finch et al. · Nature · 1992 · 1K citations

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EULAR recommendations for the management of primary small and medium vessel vasculitis

Chetan Mukhtyar, Loı̈c Guillevin, María C. Cid et al. · Annals of the Rheumatic Diseases · 2008 · 984 citations · Full text

Estimated numbers and prevalence of PI*S and PI*Z alleles of α<sub>1</sub>-antitrypsin deficiency in European countries

Ignacio Blanco · European Respiratory Journal · 2005 · 238 citations · Full text

Effect of the Z mutation on the physical and inhibitory properties of .alpha.1-antitrypsin

David A. Lomas, Dyfed L. Evans, Stuart R. Stone et al. · Biochemistry · 1993 · 228 citations

Alpha1-antitrypsin genetic polymorphism in ANCA-positive systemic vasculitis

Vincent Esnault, A. Testa, Marie Audrain et al. · Kidney International · 1993 · 218 citations

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