CONGENITAL PULMONARY STENOSIS WITH INTACT VENTRICULAR SEPTUM

Abstract

Pulmonary stenosis is one of the most important of the congenital malformations of the heart. It occurs most frequently in conjunction with a defect of the ventricular septum, dextroposition of the aorta and hypertrophy of the right ventricle (tetralogy of Fallot). It occurs also in tricuspid atresia in which there is a defect of the auricular septum and usually a defect of the ventricular septum with rudimentary right ventricle. Congenital pulmonary stenosis also occurs with intact ventricular septum. In the majority of these cases, there is an open foramen ovale. Cyanosis depends on the amount of blood shunted from right to left through the foramen ovale and on the degree of pulmonary stenosis. If there is no shunt, cyanosis is absent. In the tetralogy of Fallot and tricuspid atresia, the patient's condition may be much improved by subclavian-pulmonary¹or aortic-pulmonary anastomosis,²which permits a greater flow of blood