Proceedings of the Royal Society B Biological Sciences · 1998 · 105 citations · 43 references
Life SciencesCell BiologyMolecular BiologyDevelopmental NeuroscienceHearing ScienceOrganogenesisAuditory DevelopmentAuditory NeurobiologyAuditory NeurophysiologyCochlear FunctionCochlear NeurobiologyCochlear NeuroscienceAuditory Hair CellsAuditory Sensory EpitheliumCochlear Hair Cell RegenerationCochlear NeurophysiologyHair Cell BiologyInner Ear RegenerationMammalian Hair CellsSensory Hair Cell Development
Mammalian auditory hair cells are scarce, experimentally inaccessible, and fail to proliferate after birth or in vitro. The authors created immortal cell lines capable of differentiating into auditory hair cells to enable research, drug development, and functional studies of cochlear genes, ultimately facilitating therapeutic approaches to stimulate hair cell regeneration. The cell lines express key hair cell markers, including transcription factor Brn3.1, α9 acetylcholine receptor subunit, fimbrin, and myosins VI and VIIA. Two conditionally immortal cell lines were successfully established, each expressing at least five characteristic hair cell markers.
Mammalian auditory hair cells are few in number, experimentally inaccessible, and do not proliferate postnatally or in vitro. Immortal cell lines with the potential to differentiate into auditory hair cells would substantially facilitate auditory research, drug development, and the isolation of critical molecules involved in hair cell biology. We have established two conditionally immortal cell lines that express at least five characteristic hair cell markers. These markers are the transcription factor Brn3.1, the alpha 9 subunit of the acetylcholine receptor, the stereociliary protein fimbrin and the myosins VI and VIIA. These hair cell precursors permit functional studies of cochlear genes and in the longer term they will provide the means to explore therapeutic methods of stimulating auditory hair cell regeneration.
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Philippe Séguéla, Jacques I. Wadiche, Kelly Dineley‐Miller et al. · Journal of Neuroscience · 1993 · 1.5K citations · Full text
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