Concepedia

Protective effects of Fe-Aox29, a novel antioxidant derived from a molecular combination of Idebenone and vitamin E, in immortalized fibroblasts and fibroblasts from patients with Friedreich Ataxia

Matthias L. Jauslin, Silvia Vertuani, Elisa Durini, Lisa Buzzoni, Nunzia Ciliberti, Sara Verdecchia, Paola Palozza, Thomas Meier, Stefano Manfredini

Molecular and Cellular Biochemistry · 2007 · 21 citations · 29 references

DOI

Concepts

References

29

Friedreich's Ataxia: Autosomal Recessive Disease Caused by an Intronic GAA Triplet Repeat Expansion

Victoria Campuzano, Laura Montermini, María Dolores Moltó et al. · Science · 1996 · 2.8K citations

, , +17

Potent and specific inhibition of glutathione synthesis by buthionine sulfoximine (S-n-butyl homocysteine sulfoximine).

Owen W. Griffith, A Meister · Journal of Biological Chemistry · 1979 · 1.7K citations · Full text

, , +13

Direct observation of a free radical interaction between vitamin E and vitamin C

John E. Packer, T. F. Slater, R. L. Willson · Nature · 1979 · 1.5K citations

, , +15

Aconitase and mitochondrial iron–sulphur protein deficiency in Friedreich ataxia

Agnès Rötig, Pascale de Lonlay, Dominique Chrétien et al. · Nature Genetics · 1997 · 991 citations

, , +12

FRIEDREICH'S ATAXIA: A CLINICAL AND GENETIC STUDY OF 90 FAMILIES WITH AN ANALYSIS OF EARLY DIAGNOSTIC CRITERIA AND INTRAFAMILIAL CLUSTERING OF CLINICAL FEATURES

A E Harding · Brain · 1981 · 920 citations

, , +10