Parachordoma of Soft Tissues of the Arm

Abstract

Parachordoma, or myoepithelioma, is a very rare tumor histologically resembling chordoma but occurring in the nonaxial soft tissues. It typically has an indolent nature, with occasional late recurrence and even rare metastases. Review of existing literature reveals a male predilection, with the tumor typically occurring in the fourth decade of life in the lower extremity. It typically is managed with wide resection. We report the case of a 60-year-old woman with a right distal upper arm parachordoma treated with wide resection of the tumor.