Science · 2003 · 1.4K citations · 22 references
Life SciencesCell BiologyMolecular BiologyApoptosisCell SignalingMitochondrial BiologyApoptosis RegulationApoptotic SignalingBcl-2 Family ProteinsMitochondrial Calcium HomeostasisMitochondrial DysfunctionMitochondrial PhysiologyApoptotic Cell Death RegulationCa2+ SignalingCalcium Release From Intracellular StoresCalcium-dependent Regulation Of ApoptosisMitochondrial Apoptosis RegulationPro-apoptotic Bcl-2 ProteinsProapoptotic Bcl-2 ProteinsProapoptotic Protein Regulation
BAX and BAK are multidomain proapoptotic proteins that localize to both the mitochondria and the endoplasmic reticulum, initiating mitochondrial dysfunction. In BAX/BAK‑deficient fibroblasts, reduced ER calcium impairs mitochondrial calcium uptake and apoptosis, but restoring ER calcium with SERCA or targeting BAX to mitochondria rescues death to specific stimuli, showing that BAX/BAK function at both organelles as a critical gateway for selective apoptotic signals.
BAX and BAK are "multidomain" proapoptotic proteins that initiate mitochondrial dysfunction but also localize to the endoplasmic reticulum (ER). Mouse embryonic fibroblasts deficient for BAX and BAK (DKO cells) were found to have a reduced resting concentration of calcium in the ER ([Ca2+]er) that results in decreased uptake of Ca2+ by mitochondria after Ca2+ release from the ER. Expression of SERCA (sarcoplasmic-endoplasmic reticulum Ca2+ adenosine triphosphatase) corrected [Ca2+]er and mitochondrial Ca2+ uptake in DKO cells, restoring apoptotic death in response to agents that release Ca2+ from intracellular stores (such as arachidonic acid, C2-ceramide, and oxidative stress). In contrast, targeting of BAX to mitochondria selectively restored apoptosis to "BH3-only" signals. A third set of stimuli, including many intrinsic signals, required both ER-released Ca2+ and the presence of mitochondrial BAX or BAK to fully restore apoptosis. Thus, BAX and BAK operate in both the ER and mitochondria as an essential gateway for selected apoptotic signals.
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Proapoptotic BAX and BAK: A Requisite Gateway to Mitochondrial Dysfunction and Death
Michael C. Wei, Wei‐Xing Zong, Emily H. Cheng et al. · Science · 2001 · 3.9K citations · Full text
Bcl-2 functions in an antioxidant pathway to prevent apoptosis
David M. Hockenbery, Zoltán N. Oltvai, Xiao-Ming Yin et al. · Cell · 1993 · 3.4K citations
Programmed Cell Death Induced by Ceramide
Lina M. Obeid, Corinne M. Linardic, Linda A. Karolak et al. · Science · 1993 · 1.8K citations