Concepedia

Mitochondrial Membrane Fluidity is Consistently Increased in Different Models of Huntington Disease: Restorative Effects of Olesoxime

Janett Eckmann, Laura E. Clemens, Schamim H. Eckert, Stephanie Hagl, Libo Yu-Taeger, Thierry Bordet, Rebecca M. Pruss, Kristina Leuner, Huu Phuc Nguyen, Gunter P. Eckert

Molecular Neurobiology · 2014 · 51 citations · 66 references

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66

A novel gene containing a trinucleotide repeat that is expanded and unstable on Huntington's disease chromosomes

Marcy E. MacDonald · Cell · 1993 · 8.4K citations · Full text

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A novel gene containing a trinucleotide repeat that is expanded and unstable on Huntington's disease chromosomes. The Huntington's Disease Collaborative Research Group.

Manish A. Shah, Nicole A. Datson, Lakshmi Srinidhi et al. · Cell · 1993 · 3.1K citations

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Early mitochondrial calcium defects in Huntington's disease are a direct effect of polyglutamines

Alexander Panov, Claire‐Anne Gutekunst, Blair R. Leavitt et al. · Nature Neuroscience · 2002 · 1K citations

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Full-Length Human Mutant Huntingtin with a Stable Polyglutamine Repeat Can Elicit Progressive and Selective Neuropathogenesis in BACHD Mice

Michael A. Gray, Dyna Shirasaki, Carlos Cepeda et al. · Journal of Neuroscience · 2008 · 609 citations · Full text

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Mutant huntingtin binds the mitochondrial fission GTPase dynamin-related protein-1 and increases its enzymatic activity

Wenjun Song, Jin Chen, Alejandra M. Petrilli et al. · Nature Medicine · 2011 · 544 citations · Full text

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