Sugar-mimic glycosidase inhibitors: natural occurrence, biological activity and prospects for therapeutic application

Enzymatic Defect in Fabry's Disease

Roscoe O. Brady, Andrew E. Gal, Roy M. Bradley et al. · New England Journal of Medicine · 1967 · 1.1K citations

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Role of N-linked oligosaccharide recognition, glucose trimming, and calnexin in glycoprotein folding and quality control.

Craig Hammond, Ineke Braakman, Ari Helenius · Proceedings of the National Academy of Sciences · 1994 · 835 citations

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Accelerated transport and maturation of lysosomal α–galactosidase A in Fabry lymphoblasts by an enzyme inhibitor

Jianqiang Fan, Naoki Asano, Yoshiyuki Suzuki · Nature Medicine · 1999 · 613 citations

Life Sciences, Biochemistry, Molecular Biology +14

Association of folding intermediates of glycoproteins with calnexin during protein maturation

Weijia Ou, P.H. Cameron, David Y. Thomas et al. · Nature · 1993 · 559 citations

Life Sciences, Biochemistry, Molecular Biology +12

?-Glucosidase inhibitors

Delf Schmidt, Wolf B. Frommer, Bodo Junge et al. · Die Naturwissenschaften · 1977 · 468 citations