CARNITINE REDUCES FASTING KETOGENESIS IN PATIENTS WITH DISORDERS OF PROPIONATE METABOLISM

A simple, rapid method for the determination of glucose, lactate, pyruvate, alanine, 3-hydroxybutyrate and acetoacetate on a single 20-μl blood sample

Ronald J. Maughan · Clinica Chimica Acta · 1982 · 285 citations

Energy Metabolism, Biochemistry, Medicine +11

Urinary Excretion of l-Carnitine and Acylcarnitines by Patients with Disorders of Organic Acid Metabolism: Evidence for Secondary Insufficiency of l-Carnitine

R. A. Chalmers, Charles R. Roe, T. E. Stacey et al. · Pediatric Research · 1984 · 248 citations · Full text

Secondary Insufficiency, Urology, Urinary Excretion +4

Systemic Carnitine Deficiency — A Treatable Inherited Lipid-Storage Disease Presenting as Reye's Syndrome

P Chapoy, C. Angelini, Wendy J. Brown et al. · New England Journal of Medicine · 1980 · 246 citations

Metabolic Syndrome, Electrolyte Disorder, Hepatology +14

Fasting hypoglycemia resulting from hepatic carnitine palmitoyl transferase deficiency

P.F. Bougneres, Jean-M. Saudubray, C. Marsac et al. · The Journal of Pediatrics · 1981 · 179 citations

Metabolic Syndrome, Hepatology, Metabolic Disorder +6

L-carnitine enhances excretion of propionyl coenzyme A as propionylcarnitine in propionic acidemia.

C. R. Roe, David S. Millington, David Maltby et al. · Journal of Clinical Investigation · 1984 · 142 citations · Full text

Propionyl Coenzyme A, Steady State Nature, Aldehyde Dehydrogenase +12