Rare Combination of Duplication of Genito‐urinary Tract, Hindgut, Vertebral Column and Other Associated Anomalies

Abstract

Summary Two children, one male and one female have been presented with more or less identical rare congenital deformities of genito‐urinary tract, hindgut and vertebral column. Both the children had completely separate urinary systems, each comprising 1 kidney ureter, bladder, urethra and penis in the boy with no communication at any level. The genital organs in both cases were completely duplicated, the boy having 2 penes and double scrotum containing a normal testis in each and the girl had 2 vaginal orifices and 2 uteri as demonstrated by 2 cervices projecting into the 2 vaginae (no other test to demonstrate the 2 uteri were done). Both the children had duplication of hindgut and anorectal atresia, complete in the boy and partial in the girl. The girl also had reverse rotation of the hindgut. Both the children had defects in the vertebral column. The boy had hemivertebra, first lumbar rib on the right side and double sacrum. The girl had malformation of the sacrum with spina bifida and diastasis of pubic bones. The anomalies in the girl on the whole showed an attempt at reduplication of single organs and fusion of paired ones.