XANTHOMATOSIS (SCHÜLLER-CHRISTIAN SYNDROME)

Abstract

Henschen,1 in a monograph published in 1931, divided the cases of the Schüller-Christian syndrome into eight classes as follows: Xanthomatosis with skeletal changes, exophthalmos and diabetes insipidus. Xanthomatosis with skeletal changes and exophthalmos and without diabetes insipidus. Xanthomatosis with skeletal changes and diabetes insipidus and without exophthalmos. Xanthomatosis with skeletal changes and without exophthalmos and diabetes insipidus. Xanthomatosis with diabetes insipidus and without skeletal changes and exophthalmos. Xanthomatosis with disturbances in growth. Xanthomatosis, or xanthosarcomatosis, without skeletal changes, diabetes insipidus and exophthalmos. Xanthomatosis of the skin only, occurring in children and young adults. In the first class, he put sixteen cases, namely, those reported by: Hand²(first case); Kay³and Hand⁴(Hand's second case); Schüller⁵(second case); Christian;⁶Grosh and Stifel;⁷Alberti;⁸Thompson, Keegan and Dunn;⁹Denzer;¹⁰Kyrklund¹¹and Henschen¹(Henschen's