Treatment with inhibitors of the NF-κB pathway improves whole body tension development in the mdx mouse

Dystrophin: The protein product of the duchenne muscular dystrophy locus

Eric P. Hoffman, Robert H. Brown, Louis M. Kunkel · Cell · 1987 · 4.6K citations

Protein Function, Biochemistry, Skeletal Muscle +8

X chromosome-linked muscular dystrophy (mdx) in the mouse.

G. Bulfield, W. G. Siller, P.A.L. Wight et al. · Proceedings of the National Academy of Sciences · 1984 · 1.7K citations · Full text

Developmental Biology, Mendelian Disorder, Skeletal Muscle +11

Expression of full-length utrophin prevents muscular dystrophy in mdx mice

Jonathon M. Tinsley, Nicolas Deconinck, Rosie Fisher et al. · Nature Medicine · 1998 · 593 citations

Muscle Function, Mdx Mice, Skeletal Muscle +5

A chronic inflammatory response dominates the skeletal muscle molecular signature in dystrophin-deficient mdx mice

John D. Porter · Human Molecular Genetics · 2002 · 437 citations

Interplay of IKK/NF-κB signaling in macrophages and myofibers promotes muscle degeneration in Duchenne muscular dystrophy

Swarnali Acharyya, S. Armando Villalta, Nadine Bakkar et al. · Journal of Clinical Investigation · 2007 · 427 citations · Full text

Dmd Mouse Models, Immunology, Cell Death +18