Marjatta Son

Copper delivery to the CNS by CuATSM effectively treats motor neuron disease in SODG93A mice co-expressing the Copper-Chaperone-for-SOD

Jared R. Williams, Emiliano Trías, Pamela R. Beilby et al. · Neurobiology of Disease · 2016 · 164 citations · Full text

Overexpression of CCS in G93A-SOD1 mice leads to accelerated neurological deficits with severe mitochondrial pathology

Marjatta Son, Krishna Puttaparthi, Hibiki Kawamata et al. · Proceedings of the National Academy of Sciences · 2007 · 160 citations · Full text

Neurodegenerative Diseases, Amyotrophic Lateral Sclerosis, Mitochondrial Function +15

Disease Progression in a Transgenic Model of Familial Amyotrophic Lateral Sclerosis Is Dependent on Both Neuronal and Non-Neuronal Zinc Binding Proteins

Krishna Puttaparthi, William L. Gitomer, Uma Krishnan et al. · Journal of Neuroscience · 2002 · 111 citations · Full text

Biological effects of CCS in the absence of SOD1 enzyme activation: implications for disease in a mouse model for ALS

Jody B. Proescher, Marjatta Son, Jeffrey L. Elliott et al. · Human Molecular Genetics · 2008 · 65 citations · Full text

Neurodegenerative Diseases, Amyotrophic Lateral Sclerosis, Biological Effects +13

Isolated Cytochrome c Oxidase Deficiency in G93A SOD1 Mice Overexpressing CCS Protein

Marjatta Son, Scot C. Leary, Nadine Romain et al. · Journal of Biological Chemistry · 2008 · 46 citations · Full text