Douglas S. Kerr

Deficiency of the reduced nicotinamide adenine dinucleotide dehydrogenase component of complex I of mitochondrial electron transport. Fatal infantile lactic acidosis and hypermetabolism with skeletal-cardiac myopathy and encephalopathy.

Charles L. Hoppel, Douglas S. Kerr, Beverly Barrett Dahms et al. · Journal of Clinical Investigation · 1987 · 161 citations · Full text

Mitochondrial Defect, Lipid Peroxidation, Mitochondrial Biology +18

Deficiency of the iron-sulfur clusters of mitochondrial reduced nicotinamide-adenine dinucleotide-ubiquinone oxidoreductase (complex I) in an infant with congenital lactic acidosis.

Randall W. Moreadith, Mark L. Batshaw, T Ohnishi et al. · Journal of Clinical Investigation · 1984 · 138 citations · Full text

Energy Metabolism, Aldehyde Dehydrogenase, Biochemistry +15

Treatment of congenital lactic acidosis with dichloroacetate

Peter W. Stacpoole, Carie Barnes, M. D Hurbanis et al. · Archives of Disease in Childhood · 1997 · 112 citations · Full text

Pathology, Involve Deficiencies, Lactation +16

The Regulation of Methionine Synthesis and the Nature of Cystathionine γ-Synthase in Neurospora

Douglas S. Kerr, Martin Flavin · Journal of Biological Chemistry · 1970 · 81 citations · Full text

Cystathionine Synthase Activity, Molecular Biology, Cystathionine γ-Synthase +17

Oxidative phosphorylation analysis: assessing the integrated functional activity of human skeletal muscle mitochondria—case studies

Michelle A. Puchowicz, Marie E. Varnes, Bruce H. Cohen et al. · Mitochondrion · 2004 · 68 citations

Energy Metabolism, Mitochondrial Function, Biochemistry +14