Francesca Tonelli

Zebrafish Collagen Type I: Molecular and Biochemical Characterization of the Major Structural Protein in Bone and Skin

Charlotte Gistelinck, Roberta Gioia, Assunta Gagliardi et al. · Scientific Reports · 2016 · 129 citations · Full text

Life Sciences, Developmental Biology, Molecular Biology +14

The chaperone activity of 4PBA ameliorates the skeletal phenotype of Chihuahua, a zebrafish model for dominant osteogenesis imperfecta

Roberta Gioia, Francesca Tonelli, Ilaria Ceppi et al. · Human Molecular Genetics · 2017 · 87 citations · Full text

Medicine, Developmental Biology, Genetics +17

Severely Impaired Bone Material Quality in Chihuahua Zebrafish Resembles Classical Dominant Human Osteogenesis Imperfecta

Imke A.K. Fiedler, Felix N. Schmidt, Eva Maria Wölfel et al. · Journal of Bone and Mineral Research · 2018 · 80 citations · Full text

Medicine, Animal Sciences, Animal Anatomy +16

Crtap and p3h1 knock out zebrafish support defective collagen chaperoning as the cause of their osteogenesis imperfecta phenotype

Francesca Tonelli, Silvia Cotti, Laura Leoni et al. · Matrix Biology · 2020 · 43 citations

Medicine, Genetics, Molecular Genetics +12

Cell differentiation and matrix organization are differentially affected during bone formation in osteogenesis imperfecta zebrafish models with different genetic defects impacting collagen type I structure

Valentina Daponte, Francesca Tonelli, Cecilia Masiero et al. · Matrix Biology · 2023 · 21 citations · Full text

Medicine, Genetics, Molecular Genetics +17