Agnès Gaudry

Pathogenic mutations causing LBSL affect mitochondrial aspartyl-tRNA synthetase in diverse ways

Laura van Berge, Josta Kevenaar, Emiel Polder et al. · Biochemical Journal · 2012 · 35 citations

Genetics, Molecular Biology, Diverse Ways +16

Thermodynamic properties distinguish human mitochondrial aspartyl-tRNA synthetase from bacterial homolog with same 3D architecture

Anne Neuenfeldt, Bernard Lorber, Eric Ennifar et al. · Nucleic Acids Research · 2012 · 34 citations · Full text

Crystal Structure, Protein Assembly, Molecular Biology +19

Neurodegenerative disease-associated mutants of a human mitochondrial aminoacyl-tRNA synthetase present individual molecular signatures

C. Sauter, Bernard Lorber, Agnès Gaudry et al. · Scientific Reports · 2015 · 29 citations · Full text

Adaptation of aminoacylation identity rules to mammalian mitochondria

Aurélie Fender, Agnès Gaudry, Frank Jühling et al. · Biochimie · 2012 · 22 citations

Biochemistry, Mitochondrial Function, Natural Sciences +4

Re-designed N-terminus enhances expression, solubility and crystallizability of mitochondrial protein

Agnès Gaudry, Bernard Lorber, Anne Neuenfeldt et al. · Protein Engineering Design and Selection · 2012 · 12 citations