Mario de la Mata

Coenzyme Q<sub>10</sub> Therapy

Juan Garrido‐Maraver, Mario D. Cordero, Manuel Oropesa-Ávila et al. · Molecular Syndromology · 2014 · 144 citations · Full text

Pharmacotherapy, Clinical Treatment, Treatment Development +16

Secondary coenzyme Q ₁₀ deficiency triggers mitochondria degradation by mitophagy in MELAS fibroblasts

David Cotán, Mario D. Cordero, Juan Garrido‐Maraver et al. · The FASEB Journal · 2011 · 136 citations

Pharmacological Chaperones and Coenzyme Q10 Treatment Improves Mutant β-Glucocerebrosidase Activity and Mitochondrial Function in Neuronopathic Forms of Gaucher Disease

Mario de la Mata, David Cotán, Manuel Oropesa-Ávila et al. · Scientific Reports · 2015 · 127 citations · Full text

Pantothenate Rescues Iron Accumulation in Pantothenate Kinase-Associated Neurodegeneration Depending on the Type of Mutation

Mónica Álvarez-Córdoba, Aida Fernández Khoury, Marina Villanueva‐Paz et al. · Molecular Neurobiology · 2018 · 62 citations

Iron Metabolism, Nutritional Neuroscience, Neuroprotection +6

Critical role of AMP-activated protein kinase in the balance between mitophagy and mitochondrial biogenesis in MELAS disease

Juan Garrido‐Maraver, Marina Villanueva‐Paz, Mario D. Cordero et al. · Biochimica et Biophysica Acta (BBA) - Molecular Basis of Disease · 2015 · 52 citations

Cell Autophagy, Mitophagy, Melas Disease +11