Mice with endogenous <scp>TDP</scp> ‐43 mutations exhibit gain of splicing function and characteristics of amyotrophic lateral sclerosis

Pietro Fratta, Prasanth Sivakumar, Jack Humphrey, +39

The EMBO Journal

Late stage treatment with arimoclomol delays disease progression and prevents protein aggregation in the SOD1^G93A mouse model of ALS

Bernadett Kalmár, Sergey S. Novoselov, Anna L. Gray, +3

Journal of Neurochemistry

Cell DeathSynaptic SignalingSocial SciencesArimoclomol DelaysAlzheimer's Disease +17

Targeting protein homeostasis in sporadic inclusion body myositis

Mhoriam Ahmed, Pedro Machado, Adrian Miller, +24

Science Translational Medicine

Humanized mutant FUS drives progressive motor neuron degeneration without aggregation in ‘FUSDelta14’ knockin mice

Anny Devoy, Bernadett Kalmár, Michelle Stewart, +18

Brain

Knockout MouseNeurodegenerative DiseasesSynaptic PlasticityMolecular NeuroscienceDevelopmental Biology +13

A comprehensive assessment of the <i>SOD1G93A</i> low-copy transgenic mouse, which models human amyotrophic lateral sclerosis

Abraham Acevedo‐Arozena, Bernadett Kalmár, Shafa Essa, +10

Disease Models & Mechanisms

Knockout MouseNeurodegenerative DiseasesComprehensive AssessmentAmyotrophic Lateral SclerosisTransgenic Mouse Models +13

Inhibiting p38 MAPK alpha rescues axonal retrograde transport defects in a mouse model of ALS

Katherine L. Gibbs, Bernadett Kalmár, Elena R. Rhymes, +6

Cell Death and Disease

Activation of the heat shock response in a primary cellular model of motoneuron neurodegeneration-evidence for neuroprotective and neurotoxic effects

Bernadett Kalmár, Linda Greensmith

Cellular & Molecular Biology Letters

The effect of treatment with BRX-220, a co-inducer of heat shock proteins, on sensory fibers of the rat following peripheral nerve injury

Bernadett Kalmár, Linda Greensmith, Marzia Malcangio, +3

Experimental Neurology

HyperthermiaPeripheral Nerve InjurySensory FibersPhysiologyHeat Shock Proteins +9

Upregulation of Heat Shock Proteins Rescues Motoneurones from Axotomy-Induced Cell Death in Neonatal Rats

Bernadett Kalmár, Geoffrey Burnstock, Gerta Vrbovà, +3

Experimental Neurology

Molecular NeuroscienceDevelopmental BiologyAxotomy-induced Cell DeathNeurophysiologyMedicine +11

A method to solubilise protein aggregates for immunoassay quantification which overcomes the neurofilament “hook” effect

Ching‐Hua Lu, Bernadett Kalmár, Andrea Malaspina, +2

Journal of Neuroscience Methods

Molecular NeuroscienceCellular NeuroscienceMedicineImmunologyImmunochemistry +9